1. A case is reported which shows the typical features of osteopathia striata in all the long bones and probably in the pelvis, with the features of osteopetrosis in the skull and ribs.

2. The occurrence of longitudinal striation in osteopoikilosis and osteopetrosis is described, and the possible relationship between these two diseases and osteopathia striata is discussed.

3. The differential diagnosis is indicated.