Abstract
Aim
To determine the prevalence and distribution of pain in patients with Charcot-Marie-Tooth disease and the effects of surgery on this pain.
Methods
Members of the Charcot -Marie -Tooth International support group were sent a pain questionnaire. Data about the site, nature, frequency, severity of pain, pain triggers, methods of pain relief and the response to surgery were collected.
Results
There were 399 respondents (233 women and 166 men). The most frequently reported sites of pain were the legs (79%) and feet (77%). Ankle pain was reported by 57%. Walking and exercise were the most frequent pain triggers. Rest was the most common method of modifying pain (60 % of respondents). 32 % found analgesics effective and 39% used heat to relive their pain. The most common sites for surgery were the foot (36%) and ankle (26%). In 43% of patients undergoing foot surgery and 54% of patients undergoing ankle surgery, pain had been increased or introduced following surgery.
Conclusions
Patients with Charcot-Marie-Tooth disease experience significant inherent, and probably neuropathic, pain in addition to pain from mechanical causes. Surgery is unlikely to improve or eliminate pain in these patients. It may introduce pain in some. Surgery should be confined to the treatment of structural problems, as it is often ineffective at relieving pain.
The abstracts were prepared by Mr J. L. Barrie. Correspondence should be addressed to Mr J. L. Barrie, BOFSS Editor, Department of Orthopaedic Surgery, Blackburn Royal Infirmary, Blackburn, Lancashire BB2 3LR.
